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width="55%"><font face="Arial, Helvetica, sans-serif" size="2">Voir&nbsp;aussi&nbsp;notre                        dossier&nbsp;: &nbsp;</font></td>                     <td width="45%" bgcolor="#dbe0f5">                        <p><font face="Arial, Helvetica, sans-serif" size="2"> <a href="/html/dossiers/alcool/alcool.htm">Quand                          votre sant&eacute; trinque&nbsp;!</a><br>                         <a href="/html/dossiers/hepatites.htm">Les h&eacute;patites</a><br>                         <a href="/html/dossiers/hepatite_c.htm">H&eacute;patite                          C : un malaise national</a></font></p>                     </td>                   </tr>                 </table>                 <p align="center"><font size="2" face="Arial, Helvetica, sans-serif"><b>Cirrhoses                    du foie</b></font></p>                 <meta name="keywords" content="cirrhose du foie, ascite, hmochromatose, greffe de foie, encphalopathie hpatique, foie, alcool, alcoolisme, hpatite virale, maladie de Wilson, ascite">                 <p><img src="/Templates/images_encyclo/kesako.gif" width="157" height="25"></p>                 <p align="justify"><font size="2" face="Arial, Helvetica, sans-serif">C'est                    une maladie diffuse, chronique et irrversible du foie dont                    la dfinition est anatomique, avec l'association de trois types                    de lsions :</font></p>                 <div align="justify">                    <ul>                     <li>                       <div align="left"><font size="2" face="Arial, Helvetica, sans-serif">                          Une atteinte des cellules du foie (cellules hpatiques)&nbsp;;                          </font></div>                     </li>                     <li>                       <div align="left"><font size="2" face="Arial, Helvetica, sans-serif">                          Une fibrose&nbsp;; </font></div>                     </li>                     <li><font size="2" face="Arial, Helvetica, sans-serif"> Des                        nodules de rgnration o des cellules hpatiques essayent                        de fonctionner mais y arrivent mal car la disposition architecturale                        des nouvelles cellules n'est pas conforme  leurs fonctions.                        </font></li>                   </ul>                 </div>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">Selon                    la taille des nodules, on distingue les cirrhoses micronodulaires                    et macronodulaires.</font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif"><img src="/Templates/images_encyclo/causes_facteurs.gif" width="206" height="25"></font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">Les                    causes de cirrhoses sont nombreuses : l'alcool et l'hpatite                    virale sont nanmoins responsables de 90&nbsp;% des cirrhoses.</font></p>                 <div align="justify">                   <div align="left"><font size="2" face="Arial, Helvetica, sans-serif">                      En France, l'alcoolisme est responsable d'environ 50&nbsp;%                      des cirrhoses. </font></div>                     </div>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">La                    quantit d'alcool et la dure d'intoxication ncessaires pour                    provoquer une cirrhose semblent assez variables selon les individus.</font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">La                    cirrhose alcoolique est habituellement prcde d'une priode                    de latence qui ne se traduit que par un foie augment de volume,                     cause d&#8217;une surcharge en graisses (<a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=steatose',540,400);">statose</a>                    hpatique). Cette surcharge peut rgresser totalement si l'intoxication                    est interrompue. Il s'agit en gnral d'une cirrhose micronodulaire.</font></p>                 <div align="justify">                    <ul>                     <li><font size="2" face="Arial, Helvetica, sans-serif"> Les                        hpatites virales, surtout B et C chroniques, peuvent                        se compliquer de cirrhoses, ainsi que les hpatites mdicamenteuses                        ou toxiques. </font></li>                     <li><font size="2" face="Arial, Helvetica, sans-serif"> Une                        obstruction biliaire prolonge.</font></li>                     <li><font size="2" face="Arial, Helvetica, sans-serif"> L'<a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=hemochromatose',540,400);">hmochromatose</a>                        primitive est une affection gntique lie  un dfaut                        de rgulation de l'absorption intestinale du fer qui se                        fait de faon excessive. Le fer s'accumule dans les tissus                        et notamment dans le foie o,  la longue, il provoque une                        fibrose puis une cirrhose. Cette atteinte du foie est assez                        longtemps bien tolre et le contraste entre le gros foie                        et le peu de signes biologiques est vocateur. </font><br>                       <font size="2" face="Arial, Helvetica, sans-serif">La maladie                        est 10 fois plus frquente chez l'homme que chez la femme                        (du fait de la dperdition de fer lors des menstruations)                        et est reconnue vers 40-60 ans. </font><br>                       <font size="2" face="Arial, Helvetica, sans-serif">Les autres                        signes cliniques de la maladie sont les tmoins des dpts                        de fer dans les diffrents organes : la peau (pigmentation                        cutane), le pancras (diabte), le c&#339;ur (insuffisance                        cardiaque), les <a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=gonade',540,400);">gonades</a>                        (dficit gonadique).</font><br>                       <font size="2" face="Arial, Helvetica, sans-serif">L'examen                        de sang confirme le diagnostic (augmentation du taux de                        fer srique ou hypersidrmie, saturation de la transferrine).</font><br>                       <font size="2" face="Arial, Helvetica, sans-serif">Le traitement                        consiste essentiellement en des saignes rptes qui entranent                        la diminution des dpts de fer dans les tissus.</font></li>                   </ul>                 </div>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">Il                    existe des hmochromatoses secondaires lies  des transfusions                    rptes (apport important de fer), des <a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=anemie',540,400);">anmies</a>                    hmolytiques chroniques, une cirrhose alcoolique, une anastomose                    porto-cave.</font></p>                 <div align="justify">                    <ul>                     <li><font size="2" face="Arial, Helvetica, sans-serif"> La                        maladie de Wilson est une maladie gntique lie                         l'accumulation de cuivre dans diffrents organes : foie,                        <a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=cornee',540,400);">corne</a>,                        systme nerveux central. Le mcanisme enzymatique en cause                        est mal connu (dfaut de synthse de la cruloplasmine).                        </font><br>                       <font size="2" face="Arial, Helvetica, sans-serif">La maladie                        est reconnue en gnral chez l'enfant ou l'adolescent.<br>                       </font><font size="2" face="Arial, Helvetica, sans-serif">L'atteinte                        hpatique est caractrise par une fibrose puis une cirrhose.<br>                       </font><font size="2" face="Arial, Helvetica, sans-serif">L'atteinte                        de la corne se manifeste par un anneau brun-vert situ                         la priphrie de la corne (anneau de Kayser-Fleischer).<br>                       </font><font size="2" face="Arial, Helvetica, sans-serif">L'atteinte                        du systme nerveux central se manifeste par un syndrome                        <a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=extrapyramidal',540,400);">extrapyramidal</a>.<br>                       </font><font size="2" face="Arial, Helvetica, sans-serif">Le                        traitement consiste en l'administration d'un mdicament                        <a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=chlateur',540,400);">chelateur</a> du cuivre (pnicillamine).</font></li>                   </ul>                 </div>                 <div align="justify">                    <ul>                     <li><font size="2" face="Arial, Helvetica, sans-serif"> La                        cirrhose biliaire primitive est une affection frappant                        principalement la femme entre 40 et 50 ans. Elle semble                        lie  une obstruction des voies biliaires intrahpatiques                        dont la cause prcise est inconnue, mais probablement auto-immune.                        </font><br>                       <font size="2" face="Arial, Helvetica, sans-serif">La maladie                        dbute par un prurit qui prcde de plusieurs mois l'apparition                        d'un ictre. Le foie et la rate sont augments de volume                        et les signes de <a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=cholestase',540,400);">cholestase</a>apparaissent.</font><br>                       <font size="2" face="Arial, Helvetica, sans-serif">Le diagnostic                        repose sur la mise en vidence d'anticorps antimitochondries                        dans le srum. Le pronostic est variable. </font></li>                   </ul>                 </div>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">D'autres                    causes de cirrhose sont parfois retrouves : cirrhose cardiaque,                    schistosomiase, galactosmie etc...</font></p>                 <p align="justify"><img src="/Templates/images_encyclo/signes_maladie.gif" width="182" height="25"></p>                 <p align="left" ><font size="2" face="Arial, Helvetica, sans-serif">Il                    n'y a pas de symptme pendant longtemps.</font></p>                 <p align="left" ><font size="2" face="Arial, Helvetica, sans-serif">Cependant                    il existe parfois une fatigue, une perte d'apptit, un amaigrissement&#8230;</font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">A                    la palpation, le foie est souvent augment de volume, mais surtout                    il prsente une consistance ferme ou dure avec un bord infrieur                    &quot;tranchant&quot;. Il est en gnral indolore.</font></p>                 <p align="left" ><font size="2" face="Arial, Helvetica, sans-serif">D'autres                    symptmes peuvent dj tre nots :</font></p>                 <div align="justify">                    <ul>                     <li><font size="2" face="Arial, Helvetica, sans-serif"> Des                        signes traduisant la dfaillance du foie : lger <a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=ictere',540,400);">ictre</a>                        des conjonctives, angiomes stellaires, rythrose palmaire                        (rougeur au niveau de la paume de la main), flapping tremor                        (tremblement des mains), etc. </font></li>                     <li><font size="2" face="Arial, Helvetica, sans-serif"> Des                        signes traduisant une hypertension de la veine porte : <a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=splenomegalie',540,400);">splnomgalie</a>,                        circulation collatrale abdominale. </font></li>                   </ul>                 </div>                 <p align="justify"><img src="/Templates/images_encyclo/exam_analyses_compl.gif" width="272" height="25"></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">En                    cas de cirrhose du foie, les examens de laboratoire ne sont                    pas trs explicites. On peut voir des signes d'insuffisance                    hpatocellulaire (hypoalbuminmie, baisse de la capacit  coaguler),                    des signes inflammatoires, des signes discrets de destruction                    des cellules du foie (augmentation des <a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=transaminase',540,400);">transaminases</a>. Les phosphatases alcalines                    sont en gnral normales.</font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">Anmie,                    diminution du nombre de globules blancs et des plaquettes sont                    frquentes.</font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">La                    gastroscopie, l'chographie, cherchent des complications (varices                    &#339;sophagiennes et ulcre gastroduodnal).</font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">La                    ponction-biopsie du foie a un important intrt diagnostique                    et permet de prciser l'<a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=histologie',540,400);">histologie</a> de la cirrhose.</font></p>                 <p align="justify"><img src="/Templates/images_encyclo/evolution.gif" width="177" height="25"></p>                 <p align="left" ><font size="2" face="Arial, Helvetica, sans-serif">L'ascite                    est la complication la plus frquente.</font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">Elle                    peut s'installer rapidement ou progressivement. C'est un panchement                    liquidien dans la cavit pritonale qui se traduit lorsqu'il                    est important par la distension mate de l'abdomen. </font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">Le                    liquide est clair, de couleur jaune ple.<br>                   </font><font size="2" face="Arial, Helvetica, sans-serif">L'ascite                    s'accompagne d'une diminution de la <a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=diurese',540,400);">diurse</a> et d'&#339;dmes des membres infrieurs.<br>                   </font><font size="2" face="Arial, Helvetica, sans-serif">A                    un stade avanc, des anomalies hydrolectrolytiques apparaissent                    : baisses du sodium, du potassium et de l&#8217;azote dans le                    sang.</font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">Les                    ictres, sont galement une complication frquente. Il                    y a augmentation de la <a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=bilirubine',540,400);">bilirubine</a> libre et conjugue dans le sang. C'est un ictre mixte. </font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">Les                    infections sont trs frquentes et s'expliquent par la                    diminution des systmes de dfense anti-bactrienne. </font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">Il                    existe souvent une fivre modre dans les cirrhoses dont l'origine                    est mal connue.</font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">Les                    hmorragies digestives (hmatmses, mlna) sont des                    complications frquentes et graves. Elles relvent de trois                    grandes causes : rupture de varice &#339;sophagienne, ulcre                    gastroduodnal, gastrite hmorragique. Le diagnostic de la lsion                    qui saigne doit tre fait en urgence grce  la fibroscopie.                    Les troubles de la coagulation favorisent ces hmorragies.</font></p>                 <p align="justify" ><font size="2" face="Arial, Helvetica, sans-serif">Le                    cancer primitif du foie (hpatome) est une complication                    grave de la cirrhose. Diffrents symptmes permettent de suspecter                    l'apparition du cancer : fivre, douleurs de l'hypochondre droit                    (flanc droit), ictre trs fonc, hmorragie digestive, augmentation                    des phosphatases alcalines, augmentation des alpha-2-globulines                    et de l'alpha-f&#339;toprotine. Le diagnostic est affirm par                    l'chographie, la tomodensitomtrie et l'artriographie slective.</font></p>                 <p align="justify"><font size="2" face="Arial, Helvetica, sans-serif">L'<a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=encephalopathie',540,400);">encphalopathie</a> hpatique peut tre spontane                    ou provoque par une cause prcise (infection, hmorragie digestive,                    sdatifs, diurtiques, etc.). Le degr de l'encphalopathie                    est variable, de mme que son volution. Elle associe un &quot;flapping                    tremor&quot;, une odeur particulire de l&#8217;haleine (f&#339;tor                    hepaticus), des signes pyramidaux (<a href="javascript:void(0)" onclick="popup('/asp/glossaire/pop_up.asp?mot=Babinski',540,400);">Babinski</a>                    bilatral) et des signes extra-pyramidaux (hypertonie et roue                    dente).</font></p>                 <p align="justify"><img src="/Templates/images_encyclo/ne_pas_confondre.gif" width="182" height="25"></p>                 <p align="left"><font size="2" face="Arial, Helvetica, sans-serif">Il                    se fait avec les autres causes de gros foie : </font></p>                 <div align="justify">                    <ul>                     <li><font size="2" face="Arial, Helvetica, sans-serif"> Foie                        cardiaque d'insuffisance cardiaque </font></li>                     <li>                        <div align="left"><font size="2" face="Arial, Helvetica, sans-serif">                          Tumeurs hpatiques </font></div>                     </li>                     <li>                        <div align="left"><font size="2" face="Arial, Helvetica, sans-serif">                          Gros foie de cholestase </font></div>                     </li>                     <li>                        <div align="left"><font size="2" face="Arial, Helvetica, sans-serif">                          Amylose </font></div>                     </li>                     <li>                        <div align="left"><font size="2" face="Arial, Helvetica, sans-serif">                          Statose </font></div>                     </li>                     <li>                        <div align="left"><font size="2" face="Arial, Helvetica, sans-serif">                          Parasitose </font></div>                     </li>                     <li>                        <div align="left"><font size="2" face="Arial, Helvetica, sans-serif">                          Collagnoses, hmopathies, sarcodose&#8230; </font></div>                     </li>                   </ul>                 </div>                 <p align="justify"><img src="/Templates/images_encyclo/traitement.gif" width="97" height="25"></p>                 <p align="left"><font size="2" face="Arial, Helvetica, sans-serif">Il                    n'existe aucun traitement curatif de la cirrhose. Le traitement                    se limite :</font></p>                 <div align="justify">                    <ul>                     <li>                        <div align="left"><font size="2" face="Arial, Helvetica, sans-serif">                          Sevrage absolu en boissons alcoolises&nbsp;; </font></div>                     </li>                     <li>                        <div align="left"><font size="2" face="Arial, Helvetica, sans-serif">                          Diurtiques (spironolactone)&nbsp;; </font></div>                     </li>                     <li>                        <div align="left"><font size="2" face="Arial, Helvetica, sans-serif">                          Traitement symptomatique des complications. </font></div>                     </li>                   </ul>                 </div>                 <p align="left"><b><font color="42529d" size="2" face="Arial, Helvetica, sans-serif">La                    greffe de foie</font></b></p>                 <p align="justify"><font size="2" face="Arial, Helvetica, sans-serif">La                    transplantation hpatique est un traitement rserv dans certains                    centres spcialiss aux maladies chroniques du foie arrives                     un stade volu. </font></p>                 <p align="left"><font size="2" face="Arial, Helvetica, sans-serif">Les                    principales indications de cette chirurgie lourde sont :</font></p>                 <div align="justify">                    <ul>                     <li><font size="2" face="Arial, Helvetica, sans-serif"> Chez                        l'enfant les atrsies des voies biliaires&nbsp;; </font></li>                     <li><font size="2" face="Arial, Helvetica, sans-serif"> Chez                        l'adulte : la cirrhose biliaire primitive, la cholangite                        sclrosante primitive, certains cas d'hpatite chronique                        B ou C, les cirrhoses avec insuffisance hpatocellulaire                        svre, certaines tumeurs primitives du foie et des maladies                        mtaboliques rares (maladie de Wilson, dficit en alpha-1-antitrypsine,                        maladies de surcharge). </font></li>                   </ul>                 </div>                 <p align="justify"><font size="2" face="Arial, Helvetica, sans-serif">Aprs                    la transplantation, un traitement immunosuppresseur (corticodes,                    ciclosporine, azathioprine) est ncessaire. </font></p>                 <!-- #EndEditable -->                  <P align="center"><FONT face="Arial, Helvetica, sans-serif" size="1"><A href="/html/sante/encyclopedie/rossant.htm">                    Dr Lyonel Rossant, Dr Jacqueline Rossant-Lumbroso.</A></FONT></P>               </div>             </td>           </tr>         </table>       </div>     </td>     <td width="5">&nbsp;</td>     <td width="130" valign="top" align="right"><!-- #BeginLibraryItem "/Library/skycrapper_sante_v2.lbi" --><SCRIPT LANGUAGE="JavaScript"> document.write('<NOLAYER>'); document.write('<IFRAME SRC="http://ad.fr.doubleclick.net/adi/docdoc.fr/sky_sante;tile=3;sz=120x600;ord=' + randnum + '?" width="120" height="600" frameborder="no" border="0" MARGINWIDTH="0" MARGINHEIGHT="0" SCROLLING="no">'); document.write('<A HREF="http://ad.fr.doubleclick.net/jump/docdoc.fr/sky_sante;tile=3;sz=120x600;abr=!ie4;abr=!ie5;ord=' + randnum + '?">'); document.write('<IMG SRC="http://ad.fr.doubleclick.net/ad/docdoc.fr/sky_sante;tile=3;sz=120x600;abr=!ie4;abr=!ie5;ord=' + randnum + '?" width="120" height="600" border=0 ALT="Cliquez ici"></A>'); document.write('</IFRAME>'); document.write('</NOLAYER>'); document.write('<TABLE align="center"><TR><TD><ILAYER id="layer2" visibility="hidden" width="120" height="600"></ILAYER></TD></TR></TABLE>'); </SCRIPT>             <NOSCRIPT> <A HREF="http://ad.fr.doubleclick.net/jump/docdoc.fr/sky_sante;tile=3;sz=120x600;ord=123456789?" 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